Summative Diagnosis:
Cardiovascular phenotype: Situs inversus totalis and heterotaxy with congenital heart disease, such as dextrocardia, dual inferior vena cava (IVC), and right aortic arch (RAA)
Noncardiovascular phenotype: Situs inversus totalis as well as abnormal thoracic and abdominal organ situs anomalies associated with heterotaxy, such as dextrogastria, inverted lung lobation, and inverted liver lobation. Also observed were duplex kidneys with kidney cysts. Tracheal airway cilia are mostly immotile with some displaying hyperkinetic beat

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID	Code Description
0100	Situs inversus totalis
0110	Dextrocardia
0190	Heterotaxy syndrome
2700	Abnormal aortic arch
2720	Right aortic arch
2810	Inferior vena cava anomaly
3804	Congenital heart disease
3817	Abdominal situs ambiguous (abdominal heterotaxy)
4512	Renal malformation
4906	Non-cardiac abnormality
4907	Non-cardiac thoracic abnormality