Summative Diagnosis:
Double outlet right ventricle (DORV), transposition of the great arteries (TGA), myocardial non-compaction and aortic arch anomalies including interrupted aortic arch (IAA) and right aortic arch (RAA)

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID Code Description
0600 Double outlet right ventricle
0700 D-loop transposition of the great arteries
1250 Interrupted aortic arch
1802 Excessive myocardial trabeculation or noncompaction
2700 Abnormal aortic arch
3804 Congenital heart disease