Summative Diagnosis:
Cardiovascular phenotype: Situs inversus totalis and complex congenital heart disease associated with heterotaxy: levocardia/dextrocardia, right aortic arch (RAA), abnormal systemic venous connection including dual inferior vena cava (IVC), and hemiazygous connection.
Noncardiovascular phenotype: Situs inversus totalis and heterotaxy with abnormal thoracic and abdominal organ situs anomalies, such as dextrogastria, inverted lung lobation, left lung isomerism, malaligned sternal vertebra, and hypoplastic spleen. Cilia in tracheal airway cilia were immotile

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID	Code Description
0100	Situs inversus totalis
0110	Dextrocardia
0190	Heterotaxy syndrome
2700	Abnormal aortic arch
2720	Right aortic arch
2800	Systemic venous anomaly
2810	Inferior vena cava anomaly
2812	Inferior vena cava left sided
3237	Bronchial situs inversus
3816	Abdominal situs inversus
3817	Abdominal situs ambiguous (abdominal heterotaxy)
4100	Skeletal, skin, muscle anomaly
4239	Left bronchial isomerism
4447	Hepatic malformation
4851	Kartagener syndrome (siewart syndrome)(primary ciliary dyskinesia)
4906	Non-cardiac abnormality
4907	Non-cardiac thoracic abnormality