Summative Diagnosis:
Cardiovascular phenotype: Double outlet right ventricle (DORV) with subaortic VSD, hypoplastic pulmonary artery, right aortic arch, aberrant left subclavian artery forming incomplete vascular ring, ventricular noncompaction, biventricular hypertrophy.

Non-cardiac phenotype: Micropthalmia, malalignmed sternum

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Codes	Code Description
602	DORV + AVSD (AV canal)
1610	Atrioventricular canal (endocardial cushion defect)
1802	Common atrium
2720	Ventricular septal defect
2730	Excessive myocardial trabeculation or noncompaction
2760	Coronary fistula (arterio-venous or arterio-cameral)
4100	Inferior vena cava anomaly
4877	Abdominal situs ambiguous (abdominal heterotaxy)