Excel File Text File All mouse models of nonsyndromic deafness with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      autosomal dominant auditory neuropathy 1 Tg(CAG-Diap3)924Lesp/0 FVB/NJ-Tg(CAG-Diap3)924Lesp J:193237 View
autosomal dominant auditory neuropathy 1 Tg(CAG-Diaph3)771Lesp/0 FVB/NJ-Tg(CAG-Diaph3)771Lesp J:193237 View
autosomal dominant nonsyndromic deafness 9 Cochtm1Mrtn/Cochtm1Mrtn CBACa.129S4-Cochtm1Mrtn J:140594, J:167669 View
autosomal dominant nonsyndromic deafness 12 Tectatm2Gpr/Tecta+ involves: 129S/SvEv * C57BL/6J J:101691 View
autosomal dominant nonsyndromic deafness 12 Tectatm3.1Gpr/Tecta+ involves: 129S/SvEv J:203482 View
autosomal dominant nonsyndromic deafness 12 Tectatm4.1Gpr/Tecta+ involves: 129S/SvEv J:203482 View
autosomal dominant nonsyndromic deafness 12 Tectatm5.1Gpr/Tecta+ involves: 129S/SvEv J:203482 View
autosomal dominant nonsyndromic deafness 13 Col11a2tm1Mne/Col11a2tm1Mne FVB.129-Col11a2tm1Mne J:71948 View
autosomal dominant nonsyndromic deafness 22 Myo6em1Bcgen/Myo6+ involves: C57BL/6J * CBA/CaJ J:288210 View
autosomal dominant nonsyndromic deafness 22 Myo6sv/Myo6sv involves: B10.HA/(33NX)Sn * C57BL/6J J:29898 View
autosomal dominant nonsyndromic deafness 25 Slc17a8tm1Selm/Slc17a8tm1Selm involves: 129/Sv * C57BL/6 J:139493 View
autosomal dominant nonsyndromic deafness 36 Tmc1dn/Tmc1dn involves: STOCK Grhl3ct * M. m. molossinus J:22445 View
autosomal dominant nonsyndromic deafness 36 Tmc1dn/Tmc1dn STOCK Grhl3ct/J J:236 View
autosomal dominant nonsyndromic deafness 36 Tmc1Mhdabth/Tmc1+ C3HeB/FeJ-Tmc1Mhdabth/Ieg J:86685 View
autosomal dominant nonsyndromic deafness 41 P2rx2em1Xzl/P2rx2+ CBA/J-P2rx2em1Xzl J:315007 View
autosomal dominant nonsyndromic deafness 67 Osbpl2em1Cya/Osbpl2em1Cya C57BL/6-Osbpl2em1Cya J:324115 View
autosomal recessive nonsyndromic deafness 1A Del(14Gjb6-Cryl1)1Lmon/Del(14Gjb6-Cryl1)1Lmon C57BL/6JOlaHsd-Del(14Gjb6-Cryl1)1Lmon/Lmon J:345081 View
autosomal recessive nonsyndromic deafness 1A Gjb2tm1Ugds/Gjb2tm1Ugds
Tg(Otog-cre)1Ugds/0		 involves: 129P2/OlaHsd * C57BL/6 J:77823 View
autosomal recessive nonsyndromic deafness 1A Gjb2tm1Ugds/Gjb2tm1Ugds
Tg(Sox10-cre)1Wdr/0		 involves: 129P2/OlaHsd * C57BL/6 * CBA J:206835 View
autosomal recessive nonsyndromic deafness 1A Gjb6tm1.1Fama/Gjb6tm1.1Fama involves: 129P2/OlaHsd * C57BL/6 * SJL J:166362 View
autosomal recessive nonsyndromic deafness 1A Gjb6tm1Kwi/Gjb6tm1Kwi involves: 129P2/OlaHsd * C57BL/6 J:80917 View
autosomal recessive nonsyndromic deafness 2 Myo7admbo2/Myo7admbo2 involves: C57BL/6J J:195666 View
autosomal recessive nonsyndromic deafness 3 Myo15ash2-2J/Myo15ash2-2J involves: STOCK Rb(16.17)7Bnr J:69998 View
autosomal recessive nonsyndromic deafness 3 Myo15atm1.1Jebd/Myo15atm1.1Jebd involves: C57BL/6 * FVB/N J:226820 View
autosomal recessive nonsyndromic deafness 7 Tmc1baringo/Tmc1baringo involves: C57BL/6 J:181985 View
autosomal recessive nonsyndromic deafness 7 Tmc1dn/Tmc1dn involves: STOCK Grhl3ct * M. m. molossinus J:22445 View
autosomal recessive nonsyndromic deafness 7 Tmc1dn/Tmc1dn STOCK Grhl3ct/J J:236 View
autosomal recessive nonsyndromic deafness 7 Tmc1Mhdabth/Tmc1+ C3HeB/FeJ-Tmc1Mhdabth/Ieg J:86685 View
autosomal recessive nonsyndromic deafness 7 Tmc1nice/Tmc1nice involves: C57BL/6 J:181985 View
autosomal recessive nonsyndromic deafness 7 Tmc1stitch/Tmc1stitch involves: C57BL/6 J:181985 View
autosomal recessive nonsyndromic deafness 9 Otofdeaf5Jcs/Otofdeaf5Jcs STOCK Otofdeaf5Jcs/Kjn J:125960 View
autosomal recessive nonsyndromic deafness 9 Otoftm1Ugds/Otoftm1Ugds involves: 129S2/SvPas * C57BL/6 J:116097 View
autosomal recessive nonsyndromic deafness 12 Cdh2312J/Cdh2312J involves: C57BL/6J J:174758 View
autosomal recessive nonsyndromic deafness 12 Cdh23Jera/Cdh23Jera involves: C57BL/6 J:174130 View
autosomal recessive nonsyndromic deafness 12 Cdh23sals/Cdh23sals involves: C57BL/6J J:147149 View
autosomal recessive nonsyndromic deafness 16 Strctm1Ugds/Strctm1Ugds involves: 129S2/SvPas * BALB/c * C57BL/6 * C57BL/6J J:141421 View
autosomal recessive nonsyndromic deafness 18A Ush1cdfcr-2J/Ush1cdfcr-2J B6;129S4 J:85400 View
autosomal recessive nonsyndromic deafness 18A Ush1cdfcr-4J/Ush1cdfcr-4J 129P3/J-Ush1cdfcr-4J/J J:278662 View
autosomal recessive nonsyndromic deafness 18A Ush1cdfcr/Ush1cdfcr involves: BALB/cByJ J:85400 View
autosomal recessive nonsyndromic deafness 18B Otogvbd/Otogvbd involves: C3HeB/FeJ * C57BL/6J J:234038 View
autosomal recessive nonsyndromic deafness 22 Otoatm1Gpr/Otoatm1Gpr involves: 129S/SvEv J:192263 View
autosomal recessive nonsyndromic deafness 23 Pcdh15roda/Pcdh15roda BALB/c-Pcdh15roda J:220658 View
autosomal recessive nonsyndromic deafness 28 Triobptm1Tbf/Triobptm1Tbf C57BL/6-Triobptm1Tbf J:167947 View
autosomal recessive nonsyndromic deafness 29 Cldn14tm1Tbf/Cldn14tm1Tbf involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:85071 View
autosomal recessive nonsyndromic deafness 30 Myo3atm1.1Mckg/Myo3atm1.1Mckg C57BL/6-Myo3atm1.1Mckg J:166812 View
autosomal recessive nonsyndromic deafness 31 Whrnwi/Whrnwi involves: C57BL/6J * STOCK a Tyrp1b Myo5ad Oca2p Ednrbs J:269, J:5037, J:5538, J:77939 View
autosomal recessive nonsyndromic deafness 32 Cdc14aem1Tbf/Cdc14aem1Tbf involves: C57BL/6J J:257652 View
autosomal recessive nonsyndromic deafness 32 Cdc14atm1a(EUCOMM)Hmgu/Cdc14atm1b(EUCOMM)Hmgu involves: C57BL/6N * FVB J:257652 View
autosomal recessive nonsyndromic deafness 32 Cdc14atm1b(EUCOMM)Hmgu/Cdc14atm1b(EUCOMM)Hmgu involves: C57BL/6N * FVB J:257652 View
autosomal recessive nonsyndromic deafness 32 Cdc14atm1d(EUCOMM)Hmgu/Cdc14atm1d(EUCOMM)Hmgu involves: C57BL/6N * FVB J:257652 View
autosomal recessive nonsyndromic deafness 37 Myo6sv/Myo6sv involves: B10.HA/(33NX)Sn * C57BL/6J J:29898 View
autosomal recessive nonsyndromic deafness 39 Hgftm1.1Tbf/Hgftm1.1Tbf B6.Cg-Hgftm1.1Tbf/Tbf J:289982 View
autosomal recessive nonsyndromic deafness 39 Hgftm1Tbf/Hgftm1Tbf B6.Cg-Hgftm1Tbf/Tbf J:289982 View
autosomal recessive nonsyndromic deafness 42 Ildr1Gt(D178D03)Wrst/Ildr1Gt(D178D03)Wrst involves: 129S2/SvPas * Swiss Webster J:217755 View
autosomal recessive nonsyndromic deafness 42 Ildr1tm1(KOMP)Wtsi/Ildr1tm1(KOMP)Wtsi involves: C57BL/6N J:217755, J:221592 View
autosomal recessive nonsyndromic deafness 42 Ildr1tm1.1Lwa/Ildr1tm1.1Lwa involves: 129S6/SvEvTac * C57BL/6 J:221594 View
autosomal recessive nonsyndromic deafness 48 Cib2tm1.1Aela/Cib2tm1.1Aela involves: BALB/c * C57BL/6 * C57BL/6N J:262464 View
autosomal recessive nonsyndromic deafness 49 Marveld2tm1.1Sria/Marveld2tm1.1Sria involves: 129X1/SvJ * C57BL/6J J:201580 View
autosomal recessive nonsyndromic deafness 49 Marveld2tm1Sats/Marveld2tm1Sats B6.Cg-Marveld2tm1Sats J:261357 View
autosomal recessive nonsyndromic deafness 59 Pjvktm1Ugds/Pjvktm1Ugds involves: 129S2/SvPas * BALB/c * C57BL/6 J:111260 View
autosomal recessive nonsyndromic deafness 63 Tomtm1Btlr/Tomtm1Btlr C57BL/6J-Tomtm1Btlr J:137493 View
autosomal recessive nonsyndromic deafness 68 S1pr2stdf/S1pr2stdf involves: C57BL/6Brd * C57BL/6N J:240361 View
autosomal recessive nonsyndromic deafness 68 S1pr2tm1Ajml/S1pr2tm1Ajml either: (involves: 129S5/SvEvBrd) or (involves: 129S5/SvEvBrd * C57BL/6) J:231927 View
autosomal recessive nonsyndromic deafness 74 Msrb3tm1Hyk/Msrb3tm1Hyk involves: 129 * C57BL/6 J:206322 View
autosomal recessive nonsyndromic deafness 79 Tprnem1Pghu/Tprnem1Pghu B6.Cg-Tprnem1Pghu J:240563 View
autosomal recessive nonsyndromic deafness 88 Elmod3em1Jili/Elmod3em1Jili involves: C57BL/6 J:293683 View
autosomal recessive nonsyndromic deafness 93 Cabp2tm1b(KOMP)Mbp/Cabp2tm1b(KOMP)Mbp involves: C57BL/6N * FVB/N J:255028 View
X-linked deafness 4 Smpxem1Jgao/Smpx+ CBA/CaJ-Smpxem1Jgao J:314284 View
X-linked deafness 4 Smpxem1Jgao/Smpxem1Jgao CBA/CaJ-Smpxem1Jgao J:314284 View
X-linked deafness 4 Smpxem1Jgao/Y CBA/CaJ-Smpxem1Jgao J:314284 View
X-linked deafness 4 Smpxem2Jgao/Smpx+ CBA/CaJ-Smpxem2Jgao J:314284 View
X-linked deafness 4 Smpxem2Jgao/Smpxem2Jgao CBA/CaJ-Smpxem2Jgao J:314284 View
X-linked deafness 4 Smpxem2Jgao/Y CBA/CaJ-Smpxem2Jgao J:314284 View
      autosomal dominant nonsyndromic deafness 4A Ceacam16tm1Wzm/Ceacam16tm1Wzm BALB/cJ-Ceacam16tm1Wzm J:187537 View
autosomal dominant nonsyndromic deafness 25 Trpv4tm1Msz/Trpv4tm1Msz involves: 129X1/SvJ * C57BL/6 J:104851 View
autosomal recessive nonsyndromic deafness Atp6v1b1vtx/Atp6v1b1vtx MRL/MpJ-Atp6v1b1vtx/Kjn J:243701 View
nonsyndromic deafness Alg10bnse5/Alg10bnse5 129S6.B6-Alg10bnse5 J:209766 View
nonsyndromic deafness Klc2em1Jgao/Klc2em1Jgao involves: C57BL/6J J:345577 View
nonsyndromic deafness m12Anu/m12Anu Not Specified J:207337 View
nonsyndromic deafness Ppip5k2tm1a(EUCOMM)Wtsi/Ppip5k2tm1a(EUCOMM)Wtsi involves: C57BL/6N J:260825 View
nonsyndromic deafness Wfs1tm1Koks/Wfs1tm1Koks involves: 129S6/SvEvTac * C57BL/6J J:342760 View
Transgenes and
Other Mutations		     autosomal recessive nonsyndromic deafness 38 Phl1101/H/Phl1101/H involves: 101/H * MAI/Pas J:111682 View
autosomal recessive nonsyndromic deafness 38 Phl1101/H/Phl1101/H involves: 101/H * MBT/Pas J:111682 View

       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      autosomal dominant nonsyndromic deafness 2A Gjb3tm1Kwi/Gjb3tm1Kwi involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:68014 View
autosomal dominant nonsyndromic deafness 15 Pou4f3tm1Rsd/Pou4f3+ involves: 129S4/SvJae * C57BL/6 J:57149 View
autosomal dominant nonsyndromic deafness 65 Cdh23Ahl+/Cdh23Ahl+
Tbc1d24em4Tbf/Tbc1d24em4Tbf		 B6.Cg-Cdh23Ahl+ Tbc1d24em4Tbf J:299025 View
autosomal dominant nonsyndromic deafness 65 Tbc1d24em4Tbf/Tbc1d24em4Tbf C57BL/6J-Tbc1d24em4Tbf J:299025 View
autosomal recessive nonsyndromic deafness 86 Tbc1d24em3Tbf/Tbc1d24em3Tbf C57BL/6J-Tbc1d24em3Tbf J:299025 View