Excel File Text File All mouse models of long QT syndrome with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      Jervell-Lange Nielsen syndrome Kcne1pkr/Kcne1pkr C57BL/10J-Kcne1pkr J:64772 View
Jervell-Lange Nielsen syndrome Kcne1tm1Sfh/Kcne1tm1Sfh involves: 129S1/Sv J:77288, J:108905 View
Jervell-Lange Nielsen syndrome Kcnq1tm1Apf/Kcnq1tm1Apf involves: 129P2/OlaHsd * C57BL/6 J:110797 View
Jervell-Lange Nielsen syndrome Kcnq1tm1Kpfe/Kcnq1tm1Kpfe involves: 129S1/Sv * 129X1/SvJ * C57BL/6 J:67873 View
Jervell-Lange Nielsen syndrome Kcnq1tm2Kpfe/Kcnq1tm2Kpfe involves: 129S1/Sv * 129X1/SvJ * C57BL/6 * FVB/N J:93197 View
long QT syndrome 1 Kcnq1tm3Kpfe/Kcnq1+ involves: 129S1/Sv * 129X1/SvJ * C57BL/6 * FVB/N J:93197 View
long QT syndrome 3 Scn5atm1.1Iba/Scn5a+ involves: 129 * C57BL/6 J:266290 View
long QT syndrome 3 Scn5atm1Care/Scn5a+ FVB.129P2-Scn5atm1Care/Care J:128657 View
long QT syndrome 3 Scn5atm1Clhh/Scn5a+ involves: 129/SvEv J:186583 View
long QT syndrome 3 Scn5atm1Pec/Scn5a+ involves: Swiss J:71542 View
Transgenes and
Other Mutations
     long QT syndrome 1 Tg(Myh6-KCNQ1_i2)H02Desc/0 involves: FVB J:132483 View
long QT syndrome 1 Tg(Myh6-KCNQ1_i2)H05Desc/0 involves: FVB J:211437 View