Summative Diagnosis
Cardiovascular defects: Double outlet right ventricle (DORV), pulmonary stenosis (hypoplastic pulmonary artery), hypoplastic transverse arch, and coronary artery fistula.
Non-cardiovascular defects: Hydronephrosis, kidney cysts
Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID	Code Description
0600	Double outlet right ventricle
0602	DORV, ventricular defect committed to aorta
1610	Pulmonary stenosis
2240	Coronary arterio-venous fistula
2704	Aortic arch hypoplasia
2966	Hypoplastic main pulmonary artery
3804	Congenital heart disease
3950	{S,D,D}
4502	Hydronephrosis
4508	Polycystic kidney disease