Summative Diagnosis:
Cardiovascular defects: Persistent truncus arteriosus (PTA), double outlet right ventricle (DORV), Overriding aorta, aortic arch anomalies such as hypoplastic transverse arch, interrupted aortic arch (IAA), vascular sling

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID Code Description
0520 Truncus arteriosus type ii
1241 Transverse arch obstruction
1252 Interrupted aortic arch type b
1300 Ventricular septal defect
1432 Overriding aortic valve