Summative Diagnosis:
Cardiovascular defects: Hypoplastic right heart syndrome (HRHS) including: hypoplastic tricuspid valve, small right ventricle, and hypoplastic pulmonary artery (PA); right aortic arch

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID	Code Description
1720	Hypoplastic tricuspid valve
1821	Hypoplastic right ventricle (subnormal cavity volume)
2720	Right aortic arch