Summative Diagnosis:
Double outlet right ventricle (DORV) with subaortic ventricular septal defect (VSD), non-compaction of right ventricle (RV), and aortic arch anomalies including interrupted aortic arch (IAA)

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID Code Description
0600 Double outlet right ventricle
1250 Interrupted aortic arch
1300 Ventricular septal defect
1802 Excessive myocardial trabeculation or noncompaction
2700 Abnormal aortic arch
3804 Congenital heart disease