Summative Diagnosis:
Cardiac defects: Situs inversus totalis, and heterotaxy with complex congenital heart disease (CHD) such as double outlet right ventricle (DORV), hypoplastic right ventricle, atrioventricular septal defect (AVSD), perimembranous and muscular ventricular septal defect (VSD), hypoplastic tricuspid valve, vascular ring, and left pulmonary isomerism

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID	Code Description
0100	Situs inversus totalis
0110	Dextrocardia
1100	Atrioventricular canal (endocardial cushion defect)
1310	Ventricular septal defect, membranous
1320	Ventricular septal defect, muscular
1720	Hypoplastic tricuspid valve
1821	Hypoplastic right ventricle (subnormal cavity volume)
0190	Heterotaxy Syndrome
2760	Vascular ring
3804	Congenital heart disease
3974	{I,L,I}
0600	Double outlet right ventricle