Summative Diagnosis:
Cardiovascular phenotypes: Complex congenital heart disease associated with heterotaxy including mesocardia, dextroversion, double outlet right ventricle, atrioventricular septal defect (AVSD), right aortic arch and interrupted aortic arch (type-B), aberrant right subclavian artery, bilateral inferior vena cava (IVC), intracardiac total anomalous pulmonary venous return (TAPVR), common atrium, and hypoplastic right ventricle.

Noncardiovascular phenotype: Visceral organ situs anomalies, including situs inversus, dextrogastria,left lung isomerism, asplenia, immotile respiratory tracheal cilia.

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Codes	Code Description
140	Mesocardia
900	Totally anomalous pulmonary venous return
100	Situs inversus totalis
110	Dextrocardia
1140	Common atrium
1821	Hypoplastic right ventricle (subnormal cavity volume)
190	Heterotaxy Syndrome
2731	Aberrant right subclavian artery
3816	Abdominal situs inversus
4239	Left bronchial isomerism
4771	Asplenia
4851	Kartagener syndrome (siewart syndrome)(primary ciliary dyskinesia)
606	DORV + AVSD (AV canal)