Summative Diagnosis:
Cardiac phenotype: Unbalanced AVSD (RV dominant), hypoplastic left ventricle, and hypoplastic ascending aorta and transverse aortic arch. A HLHS variant.

Fyler Codes
The Fyler code developed by The Boston Children's Heart Foundation in Boston Children's Hospital provides a hierarchical clinical diagnosis of congenital cardiovascular defects and other disorders. These codes are used to delineate pathology in the mutant mouse models that parallel human disease and can be cross referenced to the International Pediatric and Congenital Cardiac Code (IPCCC) (http://www.ipccc.net/).

Fyler Code ID	Code Description
0300	Hypoplastic left heart syndrome
1100	Atrioventricular canal (endocardial cushion defect)
1811	Hypoplastic left ventricle (subnormal cavity volume)
2704	Aortic arch hypoplasia
1170	Common AV valve
1410	Aortic stenosis
2700	Abnormal aortic arch